A case report on Herlyn Werner Wunderlich syndrome : (uterine didelphys, obstructed hemivagina, ipsilateral renal agenesis)

Publication Date

2000

Document Type

Research

Abstract

Herlyn Werner Wunderlich Syndrome (Uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis) is a rare congenital anomaly of the female congenital tract. This anomaly is caused by lateral non-fusion of the Mullerian ducts with asymmetric obstruction. This condition is almost always associated with renal agenesis ipsilateral to the obstruction, which could be due to embryologic arrest at 8th week of gestation that simultaneously affects the Mullerian and metanephric ducts. The diagnosis of this condition is usually made after menarche but women usually are unaware of the didelphic uterus. Patient may present with various clinical symptoms such as severe dysmenorrhea, paravaginal mass, excessive foul mucopurulent discharge, and intermenstrual bleeding, all of which are dependent on the existence of uterine or vaginal communications. We report a case of a 29 year- old, nulligravid who presented with a two year history of intermittent abdominal pain. Transvaginal ultrasound revealed uterine didelphys with hematometra on the left with consideration of hematocolpos. On KUB Ultrasound, there was also the absence of the left kidney. Patient underwent Operative Laparoscopy with Fulguration of Endometriotic Implants and Excision of Transverse Vaginal Septum. The goals of management for such anomalies include the relief of symptoms as well as preservation of sexual and reproductive function. Prompt identification and treatment are necessary to avoid further complications.

This document is currently not available here.

Share

COinS